INHERITED MACULAR CYSTS
نویسندگان
چکیده
منابع مشابه
Macular cysts; a dominantly inherited affection with a progressive course.
"HOLES " at the macula are now generally assumed to be cysts in the central area-in the same way as crater-like " holes " of the disc are recognized as glial cysts at the nervehead. The cystic character of these holes is fairly obvious on ophthalmoscopic examination in some cases, and has been proved in some individual cases by slit-lamp microscopy of the fundus and by pathological examination ...
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The inherited macular dystrophies comprise a heterogeneous group of disorders characterised by central visual loss and atrophy of the macula and underlying retinal pigment epithelium (RPE). The different forms of macular degeneration encompass a wide range of clinical, psychophysical and histological findings. The complexity of the molecular basis of monogenic macular disease is now beginning t...
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PURPOSE To correlate the phenotype of four patients with inherited macular disease with the immunohistopathology of retinal tissue collected at the time of retinal pigment epithelium (RPE)-choroidal transplantation. METHODS A clinicopathologic case series describing the phenotype of four patients, including confocal immunohistochemistry and electron microscopy (EM), and the results of genetic...
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ژورنال
عنوان ژورنال: British Journal of Ophthalmology
سال: 1964
ISSN: 0007-1161
DOI: 10.1136/bjo.48.11.581